A case of Rendu-Osler-Weber disease with septal perforation treated with facial artery musculomucosal (FAMM) flap and septal dermoplasty
نویسندگان
چکیده
منابع مشابه
Repair of large nasal septal perforations using facial artery musculomucosal (FAMM) flap.
BACKGROUND Nasal septum perforations from surgical submucous resection, septoplasty, blunt trauma, and substance abuse may cause epistaxis, nasal obstruction, discharge, crusting, dryness, pain, and whistling. While small symptomatic perforations are closed with local mucosal flaps, options for closure of large symptomatic perforations are limited. A local pedicled flap, the facial artery muscu...
متن کاملOsler-Weber-Rendu syndrome: a case report with familial clustering.
Osler-Weber-Rendu syndrome, also known as hereditary hemorrhagic telangiectasia, is a rare autosomal dominant disorder manifested by telangiectases of the skin and mucous membranes and arteriovenous malformations of various organ systems. We present a case of Osler-Weber-Rendu syndrome with 11 affected members in her family.
متن کاملOsler-Weber-Rendu Syndrome.
Telangiectasia may be identified by visual inspection during physical examination of the skin and oral cavity or by endoscopy. Diagnosis is made after clinical examination and genetic testing based on the Curacao criteria: telangiectasia in the face, hands or oral cavity; recurrent epistaxis; arteriovenous malformations with visceral involvement; and a positive family history. Diagnosis is conf...
متن کاملOsler-Weber-Rendu Syndrome
Presentation Age-related penetrance is seen in HHT. [2] It does not present at birth but commonly presents with recurrent epistaxis, usually in the teenage years. People with the condition develop mucocutaneous lesions, usually involving the nasal mucosa, lips and tongue. These lesions are sharply demarcated red-purple macules, papules or spider-like lesions comprising a mat of tortuous vessels...
متن کاملOsler-Weber-Rendu syndrome.
To cite: Abangah G, Rashidbeygi M. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2013201034 DESCRIPTION A 57-year-old woman presented to the emergency department reporting of fresh rectal bleeding since 3 days ago. She had a history of spontaneous recurrent epistaxis since childhood but had never been fully evaluated. Her family history was also notable for a so...
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ژورنال
عنوان ژورنال: JOURNAL OF JAPAN SOCIETY FOR HEAD AND NECK SURGERY
سال: 2004
ISSN: 1349-581X,1884-474X
DOI: 10.5106/jjshns.14.121